Sickle Cell Disease-S Beta Zero Thalassemia
A form of sickle cell thalassemia characterized by the absence of hemoglobin A. Patients usually have severe anemia identical to that seen in sickle cell disease.
A form of sickle cell thalassemia characterized by the absence of hemoglobin A. Patients usually have severe anemia identical to that seen in sickle cell disease.
Requires further refinement.
NCIT:C98835
http://bioportal.bioontology.org/ontologies/NCIT/?p=classes&conceptid=http%3A%2F%2Fncicb.nci.nih.gov%2Fxml%2Fowl%2FEVS%2FThesaurus.owl%23C98835
Sufficient
S beta-zero, S Beta 0 Thalassemia, Sickle Cell-Beta Zero Thalassemia, Sickle Cell-Beta 0 Thalassemia, Hb S Beta 0 Thalassemia, Sickle Beta Zero Thalassemia, Hemoglobin S Beta 0 Thalassemia, Sickle Beta 0 Thalassemia